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PMID: 29458885 16 Adult-onset glutaric aciduria type I: rare presentation of a treatable disorder

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However, phenobarbital is effective and perhaps underutilized: Phenobarbital (15 mg/kg) was found to be equally effective as compared to lorazepam (0.1 mg/kg) as first-line therapy for status epilepticus in the VA-Cooperative trial

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259 Burke, B

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